Author(s): Dimitri Luz Felipe da Silva, Fernanda Ometto Pellizari, Maria Leticia Cintra, Elemir Macedo de Souza, Renata Ferreira Magalhaes and Andrea Fernandes Eloy da Costa Franca
A 65 year-old woman with a history of papules and nodules in the face and scalp since childhood, gradually increasing in number and size. The biopsy and histopathological analysis confirmed trichoepitheliomas and cylindromas. Based on histological and clinical findings, the diagnosis of Brooke-Spiegler syndrome, a rare dominantly inherited disorder, was performed.