A fourteen year old male patient with Eisenmenger’s syndrome (ES) and severe, progressive kyphoscoliosis presented for posterior spinal fusion, T2-L2. A thorough, preoperative evaluation and multidisciplinary conference was completed to discuss patient management and the very high risk nature of this procedure. The patient underwent the procedure, but decompensated with reduction of the spinal curvature, which we believe produced right ventricular compression leading to an irreversible pulmonary, hypertensive crisis. The patient expired later the same day.
Author(s): Christopher F. Tirotta, Alecia L. S. Stein, Richard G. Lagueruela